Product & ReviewsAntibodies
Nebulin Antibody
Product Details
- Cat. No.
- 251776
- Type
- Primary Antibody
- Clonality
- Monoclonal
- Host
- Mouse
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Description
Nebulin is a large muscle protein involved in maintaining the structural integrity of sarcomeres and the membrane system associated with the myofibrils. Nebulin binds and stabilizes F-actin. Defects in nebulin are the cause of nemaline myopathy type 2 (NEM2). NEM2 is a form of nemaline myopathy. Nemaline myopathies are muscular disorders characterized by muscle weakness of varying severity and onset, and abnormal thread or rod-like structures in muscle fibers on histologic examination.
Biological Information
- Clonality: Monoclonal
- Host: Mouse
- Reactivity: Chicken, Human, Mouse, Rat, Xenopus
- Antigen: Chicken breast nebulin.
- Isotype: Mouse IgG1
- Gene: P20929
Handling
- Quantity: 0.1 mg
- Storage: Store at -20°C. Minimize freeze-thaw cycles. Product is guaranteed one year from the date of shipment.
Applications
- ELISA (ELISA)
- Western Blotting (WB)